Complete Congenital Heart Block in a Neonatal Lupus Erythematosus Associated with Pulmonary Involvement without Pacemaker Implantation: A Case Report

Document Type : Case Report


1 Assistant Professor, Pediatric Cardiologist, Amirkabir Hospital, Arak University of Medical Sciences, Arak, Iran

2 Pediatric Resident, Amirkabir Hospital, Arak University of Medical Sciences, Arak, Iran

3 Assistant Professor, Neonatologist, Amirkabir Hospital, Arak University of Medical Sciences, Arak, Iran

4 Assistant Professor, Amiralmomenin Hospital, Department of Cardiac Surgery, School of Medicine, Arak University of Medical Sciences, Arak, Iran


Background: Neonatal lupus erythematosus is an uncommon disease. Congenital complete heart block (CCHB) usually happens in neonates with maternal systemic lupus erythematosus. The most prevalent presentation of CCHBis bradycardiathatcanbediagnosed through an electrocardiogram.
Case report: Here in, we present the case of a full-term male neonate with gestational age of 37 weeks and birth weight of 2200 g, whose mother had positive anti-Ro/SSA antibodies. The mother was asymptomatic without any criteria of systemic lupus erythematosus. The newborn presented with bradycardia, respiratory distressand narrow QRS complex without structural heart disease. He was connected to mechanical ventilator and did not need pacemaker implantation.
Conclusion: This case report was conducted on a newborn with CCHB associated with pulmonary disorder. The newborn was intubated due to respiratory distress and did not need pacemaker implantation; however, after 8-month follow up, excellent outcomes were observed. It seems that atelectasis and mechanical ventilation can intolerance, and pacemaker implantation did not need in NLE with CCHB with narrowing QRS complex.


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