Iranian Journal of Neonatology

Iranian Journal of Neonatology

Pulmonary Valvar Stenosis from the Fetal to the Infantile Period: A Case Report

Document Type : Case Report

Authors
Mohammad Reza Khalilian 1
Hassan Zamani 2
Soraya Salehgargari 3
Hossein Tavallai 4
Mohammad Ghazavi 5
Hooman Daryoshi 6
1 Department of Pediatrics, School of Medicine, Modarres Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran
2 Modarres Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran
3 Men's Health and Reproductive Health Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran
4 Shahid Beheshti University of Medical Sciences
5 Department of Pediatrics, School of Medicine, Kashan University of Medical Sciences and Health Services, Kashan, Iran
6 Department of Pediatrics, Kermanshah University of Medical Sciences, Kermanshah, Iran
10.22038/ijn.2022.52707.1944
Abstract
Background: Fetal echocardiography is a useful tool for diagnosing fetuses with congenital heart diseases, and it is best to be conducted between 17 and 19 weeks of gestational age. However, fetal echocardiography can be performed at other ages of pregnancy for a variety of reasons. This study describes one fetus with pulmonary valvar stenosis based on the fetal echocardiogram in the uterus.
Case report: This study describes one fetus with pulmonary valve stenosis based on the fetal echocardiogram in the uterus. We referred the family to a hospital with neonatal intensive care unit admission. After birth, we followed her serially and confirmed pulmonary valve stenosis, which increased in severity after two months. Subsequently, we performed a percutaneous balloon valvuloplasty.
Conclusion: Our findings showed that some cardiac defects could vary in severity during pregnancy and post-birth. There was clear evidence that pulmonary valvar stenosis was a lesion developed during the fetus's lifetime to tolerate the lesion. Although pulmonary stenosis progressed in the early months after birth, it was easily treated through balloon angioplasty.
 
 
Keywords
Fetal
Infantile
Pulmonary stenosis
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Iranian Journal of Neonatology
Volume 13, Issue 1
Winter 2022
Pages 74-78