Second-degree Atrioventricular (Mobitz 1) Heart Block in a 52-hour-old Newborn: A Very Rare Case Report

Document Type : Case Report

Authors

1 Neonatal and Children Health Research Center, Golestan University of Medical Sciences, Gorgan, Iran

2 Neonatal and Children Health Research Center, Golestan University of Medical Sciences, Gorgan, Iran/Bone, Joint, and Related Tissue Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran

Abstract

Background: Cardiac conduction disorders are rare syndromes in neonates and children. According to the literature atrial septal defect, especially ostium secundum type, is associated with atrioventricular (AV) block. Wenckebach conduction heart block is very rare in a neonate; however, there is a dearth of research on the prevalence of this type of heart block regarding the neonates and pediatrics literature. This disorder has only been addressed earlier in thalassaemia major and dengue fever in Pediatrics. There have been different anatomical and metabolic and genetic etiologies for this condition. Wenckebach block is a gradual delay in sending the electrical signal from the sinoatrial node to the ventricles with each beat until there is a single dropped beat, which could be uneventful or problematic later in life. This study aimed to present a deep investigation of a rare case of congenital Wenckebach conduction heart block.
Case report: The case in this study was a 52-hour-old female neonate who was diagnosed to suffer from Mobitz type 1 or Wenckebach heart block possibly due to a small ostium secundum atrial septal defect. Therefore, it was suggested to provide supportive care and regular follow-up visit.
Conclusion: Precise antenatal care and investigation are required to reduce the morbidity and mortality rate of such condition.

Keywords

References

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Iranian Journal of Neonatology
Volume 10, Issue 1
March 2019
Pages 89-92

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