Iranian Journal of Neonatology

Iranian Journal of Neonatology

Navigating the Challenges of Neonatal Type 2 CPAM: A Case Study of Successful Pneumonectomy and Intensive Care

Document Type : Case Report

Authors
Masayu Amanda Ledika 1
Tetty Yuniaty 1
Aris Primadi 1
Fiva Apirilia Kadi 1
Hasrayati Agustina 2
Citra Yulia Sari 1
1 Department of Pediatrics, Faculty of Medicine, Padjadjaran University, Dr. Hasan Sadikin General Hospital, Bandung, West Java 40161, Indonesia
2 Department of Pathology Anatomy, Padjadjaran University, Dr. Hasan Sadikin General Hospital, Bandung, West Java 40161,
10.22038/ijn.2026.87641.2687
Abstract
Background: Congenital Pulmonary Airway Malformation (CPAM) is a rare problem in the development of the fetal tracheobronchial tree. If it is not treated properly, it can cause serious illness and even death. This report documents and emphasizes the challenges associated with postnatal CPAM diagnosis, the risks of significant surgical intervention, and the importance of meticulous clinical management to achieve the best possible patient outcomes.
Case Report: This case report details the condition of a 14-day-old male neonate diagnosed with Type II CPAM, a collapsed area in his left lung, pneumonia, ASD, and VSD. The patient underwent surgery to remove his left lung on the 19th day after birth (5 days after admission). Chest tubes were placed after the operation. Although he experienced some complications after surgery, he gradually improved and was discharged 42 days after the surgery.
Conclusion: Early surgery for symptomatic CPAM can lead to good outcomes, even in the presence of serious complications. To achieve the best results, it is important to have a multidisciplinary team, robust infection control, and long-term follow-up, especially in places with limited resources.
 
Keywords
Congenital pulmonary airway malformation
CPAM
Neonate
Resection surgery
Respiratory distress
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Iranian Journal of Neonatology
Volume 17, Issue 2
Spring 2026
Pages 50-58